Epidermolysis Bullosa Acquisita Presenting a Mix of Classical and Atopiform Features

Authors: Somani VK*, Somani A, Reddy IS and Annabathula A

DOI: 10.23880/cdoaj-16000311

Volume 8, Issue 3

Abstract

Epidermolysis bullosa acquisita (EBA) is a rare acquired autoimmune bullous disorder. This disease is characterised by the presence of autoantibodies targeted against Collagen VII of the anchoring fibrils in the basement membrane zone of skin and mucous membranes. The two most common presentations of EBA are the classical or mechano-bullous and the bullous pemphigoid (BP) like forms. Patients with BP-like form of EBA have generally profuse skin lesions suggestive of BP in some areas and EBA in others. We present a case of inflammatory BP like EBA, in a young woman, who presented with classical and also atypical atopiform features.

Keywords: Epidermolysis Bullosa Acquisita; Xerosis; Lichenification; Atopiform

View PDF