Retinitis Pigmentosa with Bilateral Ectopia Lentis

Authors: Krishnagopal Srikanth

DOI: 10.23880/oajo-16000307

Volume 9, Issue 1

Abstract

Retinitis pigmentosa (RP), a degenerative disorder characterized by a diverse array of ocular and systemic manifestations, was initially reported in 1857. Despite over a century of research, zonular weakness in RP still remains unsolved. We report a late presentation of bilateral inferior subluxation of lens, with visible zonular fibres. The patient exhibited no systemic abnormalities suggestive of a syndromic presentation. This appears to be a rare instance of bilateral concurrent spontaneous ectopia lentis (EL) associated with RP, with no syndromic association. It serves as a wake-up call for urgent need of further research in understanding the aetiology of RP.

Keywords: Retinitis Pigmentosa; Ectopia Lentis; Night Blindness; Post-Operative Lens Dislocation; Ocular Examination

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