ISSN: 2578-465X
Morning Glory Syndrome: A Case Report
Authors:
Kouassi FX1*, Koman CE1, Diomandé IA2, Somahoro M1, Sowagnon TYC1, Kra ANS1 and Koffi KV2
Introduction: Morning Glory Syndrome is a congenital anomaly of the papilla. It is uncommon, and can be isolated or associated with other ocular or general malformations. The aim of this observation was to report the first case of Morning Glory Syndrome in Côte d'Ivoire associated with hypertelorism and agenesis of the nasal pyramid.
Observation: we present an 8-year-old male child with no particular history admitted in consultation for exotropia of the left eye that had been developing for 6 months. On examination, the left eye had a visual acuity reduced to a luminous perception and had a normal anterior segment. In the eye fundus, there was a large papilla excavated in the center, partly filled by a glial proliferation with a raised ring of pigments around the excavation and an abnormal disposition of the vessels, evoking Morning Glory Syndrome. The right eye was unremarkable. The examination of the oculomotricity revealed an intermittent exotropia of the left eye. In addition, there was hypertelorism, nystagmus in the left eye and agenesis of the nasal pyramid.
Discussion: Morning Glory Syndrome is an uncommon congenital disorder characterized by a widely enlarged papilla, pink-orange in color, with a small glial tuft in the center. The retinal vessels are arranged radially in relation to the papilla. A pigmented ring surrounds the excavation. The incidence is not well known. It is generally unilateral. It is discovered in children most often on the occasion of visual impairment, nystagmus, strabismus and, more rarely, leukokoria. However, in some cases, the discovery may be fortuitous in case of systematic clinical examination in children or adults.
Conclusion: This papillary anomaly requires the search for associated general and / or ocular malformations. Surveillance is necessary given retinal detachment risk. Early screening followed by a management in a better time of organic abnormalities of the optic nerve is also essential in order to avoid deep amblyopia.
Keywords:
Morning Glory Syndrome; Papillary anomaly; Strabismus; Amblyopia; Leukokoria
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