Anesthesia for Pulmonary Artery Bending and Patent Ductus Arteriosus Ligation with Miller-Dieker Syndrome Infant

Authors: Ki-jae Lee, Keun Hyeong Lee, Ye Sull Kim, Taewon Lee, Deokkyu Kim, Sang-Kyi Lee, Jeongwoo Lee and Jun Ho Lee*

DOI: 10.23880/accmj-16000162

Volume 4, Issue 4

Abstract

Miller-Dieker syndrome (MDS) is a rare disorder characterized by type I lissencephaly (smooth brain) and characteristic facial features including protruding foreheads, depressed temples, low-necked, protruding upper lip, and small jaws. Many MDS patients have congenital heart defect and growth retardation. If these MDS cases are accompanied by deformities such as VSD, palliative treatment may be needed to prolong life. There is a case report of general anesthesia in children with MDS undergoing laryngotracheal separation and percutaneous gastrostomy surgery. However, anesthetic management of correcting heart anomalies has not been reported. The authors faced an infant with MDS who requires emergent pulmonary artery bending and Patent ductus arteriosus (PDA) ligation, and performed general anesthesia. We describe a case of MDS patient who had correcting heart anomalies and review the anesthetic management of MDS.

Keywords: Miller-Dieker syndrome; Difficult airway; Congenital heart anomaly

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