Hepatosplenic T Cell Lymphoma: A Rare Disease

Authors: Iffat Jamal

Volume 4, Issue 1

Abstract

Hepatosplenic T cell lymphoma (HSTCL) is an uncommon neoplasm comprising 5% of peripheral T-cell lymphomas. We report an uncommon case of Peripheral T-cell lymphoma that is characterized by primary extranodal disease with malignant T cell proliferation in spleen, liver and bone marrow. 19 year old male patient presented with fever, weakness and pain abdomen for 2 months. On clinical examination he was pale and had massive hepatosplenomegaly. The diagnosis was quite challenging as thorough clinical, hematological and immunophenotypic correlation was required.

Keywords: Hepatosplenic; Gamma-delta receptor; Bone marrow; Immunophenotypic; Biopsy

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