Pulmonary Arterial Hypertension Associated Systemic Sclerosis

Authors: Attapon C and Ruangrong C

DOI: 10.23880/oajprs-16000107

Volume 2, Issue 1

Abstract

Pulmonary hypertension (PAH) affects up to 12 % of patients with systemic sclerosis (SSc), with mortality rate of 50 % within 3 years. Patients with SSc-associated PAH (SSc-PAH) have three times increased risk of death, compared to idiopathic PAH (IPAH). SSC-PAH patients may receive a diagnosis late in the course of disease due to insidious onset and the high prevalence of musculoskeletal, cardiac, and pulmonary parenchymal comorbidities.

Keywords: Pulmonary; Arterial Hypertension; Systemic Sclerosis

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