The Benignant Lymphatic-Acquired Progressive Lymphangioma

Authors: Bajaj A*

DOI: 10.23880/cdoaj-16000232

Volume 6, Issue 1

Abstract

Benign lymphangioendothelioma is an extremely exceptional lymphatic, vascular proliferation which morphologically recapitulates adjunctive malignant, vascular neoplasms. The complex, vascular hamartoma is comprised of three distinctive components denominated as lymphatic vessels, blood vessels and smooth muscle. Essentially a vascular lesion of lymphatic origin, the condition demonstrates focal, benign proliferation of lymphatic vessels accompanied by localized soft tissue infiltration. The disorder was initially scripted by Wilson Jones in 1964 and is additionally designated as “acquired progressive lymphangioma” or benign lymphoendothelioma. The uncommon, benign, vascular proliferation layered with endothelial cells immune reactive to D2-40 can simulate well differentiated angiosarcoma or patch stage Kaposi’s sarcoma. Appropriate characterization of the neoplasm is challenging and the condition can be misinterpreted as cutaneous low grade angiosarcoma.

Keywords: Neoplasm; Lymphangioma; Benign lymphangioendothelioma

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