Diastematomyelia in Children in 12 Cases and Literature Review

Authors: Bouchenaki F*, Habchi N, Bouallag M, Boustil K, Benachour MS and Bakhti S

DOI: 10.23880/nnoaj-16000163

Volume 6, Issue 2

Abstract

Introduction: Diastematomyelia is a rare form of firm spina with an incidence of 2-4 per 1,000 births that requires early diagnosis and management to avoid any neurological or orthopedic worsening that may become permanent in a growing child. Patients and Method: it is a retrospective study of 12 patients treated between January 2017 and February 2020. Results: the average age was 4.5 years with extremes ranging from 06 months to 14 years. The lumbar location being the most frequent in 8 cases (66.66%). The MRI made it possible to make the diagnosis and to classify it in type 1 in 9 cases (75%) and in type 2 in 3 cases (25%) and to highlight associated lesions in 10 cases (83.33%). All of our patients were operated on, there is 1 case of motor worsening (8.3%) which was only transient, 7 patients stabilized (58.3%) and 4 patients improved (33.33%). Conclusion: the cutaneous stigmata associated with progressive congenital scoliosis in a child should prompt us to further explorations of the entire nervous axis in search of this pathology which is associated with other nerve damage which must be treated simultaneously than Diastematomyelia.

Keywords: Diastematomyelia; Spur; Cutaneous Stigmata and Complications

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