Inflammatory Myofibroblastic Tumor of Lacrimal Gland Rare Tumor in Rare Location in Different Age Groups

Authors: Roy SR* , Biswas SK and Anjum R

DOI: 10.23880/oajo-16000339

Volume 10, Issue 1

Abstract

Inflammatory myofibroblastic tumor IMT is a rare mesenchymal neoplasm graded as intermediate biological potential. The head and neck region constitute only 5% of IMT and orbit is the rarest anatomical site of this region. In literature, most cases are reported from abdomen followed by lungs. No age is immune for IMT but has special predilection for children and young adults without any sex preference. The present article reports two cases and one case was a 2 years old baby girl who presented with complete ptosis with proptosis of right eye. Another patient was a 50-years old lady who presented with fullness of left upper eye lid along with mild ptosis. In both cases lacrimal gland was the location of tumor. Patients were well managed surgically and tumor did not recur in 3 years of their follow up. Though it is a rare tumor of orbit, it should be a differential in any inflammatory mass lesion. Surgically well managed cases reduce the recurrence rate and ensure eye salvage

Keywords: Inflammatory Myofibroblastic Tumor; Orbit; Inflammatory Cells; Lacrimal Gland; Surgical Management; Immunohistochemistry

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